DÄ internationalArchive19/2010Recurrent Episodes of Sudden Acute Sensorineural Hearing Loss
LNSLNS We wish to point out that in otological terms, Cogan’s syndrome presents primarily as recurrent, sometimes bilateral, episodes of sudden acute sensorineural hearing loss. These episodes, which may improve initially after intravenous administration of steroids, may result in progressive hearing loss and permanent surdity. In such a scenario, a cochlear implant is the only option to restore a patient’s hearing. We also ask that current terminology be used regarding surdity (“loss of hearing” rather than “deafness” [Box 2], Muckle-Wells syndrome).
DOI: 10.3238/arztebl.2010.0349a

Prof. Dr. med. Dr. h. c. med. K. B. Hüttenbrink
Dr. med. Dr. rer. nat. Julia Vent, PhD
Universitätsklinik, HNO
Kerpener Str. 62, 50937 Köln, Germany
Julia.vent@uk-koeln.de
1.
Fugate JE, Smith JH, Claassen DO: Bilateral cochlear enhancement in cogan syndrome. Neurology 2009; 73(1): 75. MEDLINE
2.
Strathmann S, Burmester GR, Rüther K, Olze H: Cogan-I-Syndrom: Eine seltene Differenzialdiagnose bei progredienter Innenohrschwerhörigkeit. Laryngo-Rhino-Otol 2009; 88: 477–8. MEDLINE
3.
Grotz W, Baba HA, Becker JU, Baumgärtel MW: Hypocomplementemic urticarial vasculitis syndrome—an interdisciplinary challenge. [Hypokomplementämisches Urtikaria-Vaskulitis-Syndrom – Eine interdisziplinäre Herausforderung]. Dtsch Arztebl Int 2009; 106: 756–63. VOLLTEXT
1. Fugate JE, Smith JH, Claassen DO: Bilateral cochlear enhancement in cogan syndrome. Neurology 2009; 73(1): 75. MEDLINE
2. Strathmann S, Burmester GR, Rüther K, Olze H: Cogan-I-Syndrom: Eine seltene Differenzialdiagnose bei progredienter Innenohrschwerhörigkeit. Laryngo-Rhino-Otol 2009; 88: 477–8. MEDLINE
3. Grotz W, Baba HA, Becker JU, Baumgärtel MW: Hypocomplementemic urticarial vasculitis syndrome—an interdisciplinary challenge. [Hypokomplementämisches Urtikaria-Vaskulitis-Syndrom – Eine interdisziplinäre Herausforderung]. Dtsch Arztebl Int 2009; 106: 756–63. VOLLTEXT