DÄ internationalArchive6/2022Synovial Chondromatosis—Reichel Syndrome

Clinical Snapshot

Synovial Chondromatosis—Reichel Syndrome

Dtsch Arztebl Int 2022; 119: 87. DOI: 10.3238/arztebl.m2022.0008

Traub, F; Farah, G; Kreitner, K

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A 27-year-old man presented with painful progressive loss of mobility in the left hip joint. Radiography revealed multiple roundish, lentil-sized periarticular densities with homogeneous calcification. The Figure shows the typical findings of synovial chondromatosis, a disease that is diagnosed more frequently in men (2:1) in the age group of 20 to 40 years. The knee is the joint most commonly affected, followed by elbow, hip, shoulder, and ankle. Biarticular manifestations are extremely rare and usually symmetrical. The pathogenesis is uncertain; maldifferentiation of the joint-forming mesenchyma with transformation of fibroblasts to chondroblasts has been postulated. Open and/or arthroscopic resection of the chondromas is indicated. Synovectomy is recommended to minimize the recurrence rate, however, studies have failed to prove a superiority of surgery over radiotherapy (radiosynoviorthesis/percutaneous irradiation). We performed open removal of the loose joint bodies with partial synovectomy, followed 6 weeks later by radiosynoviorthesis. The patient currently has no symptoms.

Prof. Dr. med. Dr. rer. nat. Frank Traub Ph.D., George Farah, Prof. Dr. med. Karl-Friedrich Kreitner
Universitätsmedizin Mainz, der Johannes Gutenberg-Universität Mainz, Frank.Traub@unimedizin-mainz.de

Conflict of interest statement: The authors declare that no conflict of interest exists.

Translated from the original German by David Roseveare.

Cite this as: Traub F, Farah G, Kreitner KF: Synovial chondromatosis—Reichel syndrome. Dtsch Arztebl Int 2022; 119: 87. DOI: 110.3238/arztebl.m2022.0008